Patients with MCAD
deficiency should not go too long without eating. They have to avoid
that their body would start to break down body fat for energy.
An adult patient is
recommended not to fast longer that 12 hours, which is a typical
children should not be allowed to fast for even shorter periods,
because their bodies will more quickly switch to breaking down body
The following table shows
the maximum fasting periods:
|| Maximum fasting period (h)
– 6 months
|| 3 – 4 gradually towards 8
|6 – 12 months
– 2 years
> 2 years
Very young children need a nightly feeding.
After that the nightly
feeding can be replaced by a late night snack rich in carbohydrates.
corn starch (in Belgium known under the brand name of Maizena Plus)
contains a lot of slow carbohydrates. Adding this to the late night
snack can help to maintain blood sugar levels during the night.
If a patient is ill and can
not eat, vomits or has a fever,
specific precautions have to be taken. See also the page about emergencies.
Read further about the low fat diet >